Hb Southampton [B106(G8)Leu→PRO, CTG→CCG] in a Uruguayan woman

نویسندگان

  • Julio Abayuba da Luz Pereira
  • Pablo López
  • Fernando Ferreira Costa
  • Mónica Sans
  • Maria de Fatima Sonati
چکیده

Hemoglobin Southampton (also known as hemoglobin Casper) is a rare hemoglobin structural variant resulting from a substitution of a leucine residue for proline at codon beta106 [beta106(G8)Leu→Pro, CTG→CCG]. It is very unstable and associated with severe hemolytic anemia. We detected this mutation in a 37-year-old Uruguayan woman with a history of severe chronic hemolytic anemia since her childhood. According to our knowledge this is the first time that this variant has been found in the Uruguayan population.

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عنوان ژورنال:

دوره 35  شماره 

صفحات  -

تاریخ انتشار 2013